J Med Assoc Thai 2000; 83 (12):1541

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Persistent Mullerian Duct Syndrome in Adult : A Case Report
Sunpaweravong S Mail, Pripatnanont C

A twenty-eight year old phenotypically and genotypically normal male adult was
admitted with a right inguinal hernia, a right retractile testis and left cryptorchidism. During
surgery, he was found to have a uterus in the right spermatic cord and a left undescended testis
(intra abdominal type). The uterus was excised, left orchidectomy, right orchidoplexy and right
herniorrhaphy were performed. This rare case is reported as persistent Mullerian Duct Syndrome
(PMDS) which is caused by impaired action of Mullerian Inhibiting Substance (MIS) in
regressing the Mullerian duct.
Key word : Persistent Mullerian Duct Syndrome, Mullerian Inhibiting Substance

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