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Case ReportOpen Access
Proteus Syndrome : A Case Report
Pangkanon S 
,
Limpongsanurak W ,
Sangtawesin V
,
Limpongsanurak W ,
Sangtawesin V Proteus syndrome is a rare genetic disorder, characterized by partial gigantism of the
hands and/or feet, asymmetry of the limbs, plantar hyperplasia, multiple hamartomatous subcuta-
neous tumors, hyperostoses, and long bone overgrowth. A one day old Thai male infant is
reported with macrosomia, hemihypertrophy of the left side of the face and left leg, large feet,
macrodactyly of toes, plantar hyperplasia, large subcutaneous mass with a violet-red surface over
the left side of the chest wall and a large port-wine stain involving the lateral aspect of the right
chest wall. The clinical findings, diagnostic criteria, differential diagnosis, and management of
the Proteus syndrome are reviewed.
Key word : Proteus Syndrome, Case Report
hands and/or feet, asymmetry of the limbs, plantar hyperplasia, multiple hamartomatous subcuta-
neous tumors, hyperostoses, and long bone overgrowth. A one day old Thai male infant is
reported with macrosomia, hemihypertrophy of the left side of the face and left leg, large feet,
macrodactyly of toes, plantar hyperplasia, large subcutaneous mass with a violet-red surface over
the left side of the chest wall and a large port-wine stain involving the lateral aspect of the right
chest wall. The clinical findings, diagnostic criteria, differential diagnosis, and management of
the Proteus syndrome are reviewed.
Key word : Proteus Syndrome, Case Report
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