Left ventricular noncompaction (LVNC) is a rare cardiomyopathy resulting from abnormal arrest during endomyocardial embryogenesis. The authors present a 6-month-old infant with intractable cardiogenic shock and echocardiographic features of LVNC, characterized by excessively prominent ventricular trabeculation and deep intertrabecular recesses as the first case report in Thailand.

Keywords: Left ventricular noncompaction, Cardiomyopathy, Heart failure, Arrhythmia, Embolization