Intestinal neuronal dysplasia is one of the most commonly encountered variant of Hirschsprung’s disease but also in that untreated cases may prove fatal. The authors describe the operative treatment for a newborn who was diagnosed with long segmental intestinal neuronal dysplasia, as the remains of the normal bowel was no more than 35 centimeters from the DJ junction. The side-to-side enteroenterostomy of the affected intestine with Santulli enterostomy could rescue the baby from
parenteral nutrition, regaining normal oral feeding.

Keywords: Intestinal neuronal dysplasia, Neuronal intestinal dysplasia, IND, NID