Hepatolithiasis is well known to represent an etiology of cholangiocarcinoma. The average age of
patients with a diagnosis of cholangiocarcinoma that occurs as a complication of hepatolithiasis is about 62
years old. Here, the authors present a case of cholangiocarcinoma that occurred in a 24-year-old woman who
presented with the recurrent cholangitis from hepatolithiasis. Left hepatectomy with hepaticojejunostomy was
performed because she had multiple stones in an atrophic left lobe of the liver. Histopathological examination
revealed that it was cholangiocarcinoma located in the inflammatory left hepatic duct.

Keywords: Bile ducts, Intrahepatic, Cholangiocarcinoma, Cholelithiasis, Cholestasis, Intrahepatic, Gallstones,
Lithiasis