Extraskeletal Ewing’s Sarcoma of the Scapula: A Case Report and Literature Review
Kanchana Leerunyakul MD1, Teerapat Ungtrakul MD, MSc2, Narongchai Teerayathanakul MD1, Pichaya Thanindratarn MD1
Affiliation : 1 Chulabhorn Hospital, HRH Princess Chulabhorn College of Medical Science, Chulabhorn Royal Academy, Bangkok, Thailand 2 Faculty of Medicine and Public Heatlh, HRH Princess Chulabhorn College of Medical Science, Chulabhorn Royal Academy, Bangkok, Thailand
Background : Extraskeletal Ewing’s sarcoma [EES] is an unusual aggressive malignant tumor that is neuroectodermal cell in
origin. Presentation in the scapula region is extremely rare. We herein present a case report and literature review of EES of the
scapula.
Case Report : An 18-year-old Thai female patient presented with a 1-year history of a gradual swelling on her right scapula
that had rapidly progressed during the past 2 months. The patient was subsequently diagnosed with EES with pulmonary
metastases. She received multi-agent chemotherapy and underwent debulking surgery. Despite this aggressive treatment, her
clinical condition worsened and she died of pulmonary metastasis.
Conclusion : EES of the scapula is rare, and knowledge regarding therapy for this condition is still limited. Despite multimodal
treatment approaches including surgery, multi-agent chemotherapy, and radiation, the prognosis remains poor.
Keywords : Extraskeletal Ewing’s Sarcoma, Scapula, Bone cancer
